{"created":"2024-11-29T10:18:51.122827+00:00","id":2001877,"links":{},"metadata":{"_buckets":{"deposit":"c84c579e-01b8-4bb2-b3d6-3188bbdb765f"},"_deposit":{"created_by":8,"id":"2001877","owners":[8],"pid":{"revision_id":0,"type":"depid","value":"2001877"},"status":"published"},"_oai":{"id":"oai:fmu.repo.nii.ac.jp:02001877","sets":["1732778801467:1732778962699:1732874517304"]},"author_link":[],"item_1617186331708":{"attribute_name":"Title","attribute_value_mlt":[{"subitem_title":"A case of a child with sle presenting with hps as a primary manifestation","subitem_title_language":"en"}]},"item_1617186419668":{"attribute_name":"Creator","attribute_type":"creator","attribute_value_mlt":[{"creatorNames":[{"creatorName":"Ono, Atsushi","creatorNameLang":"en"}]},{"creatorNames":[{"creatorName":"Kawasaki, Yukihiko","creatorNameLang":"en"}]},{"creatorNames":[{"creatorName":"Kanno, Syuto","creatorNameLang":"en"}]},{"creatorNames":[{"creatorName":"Ohara, Shinichiro","creatorNameLang":"en"}]},{"creatorNames":[{"creatorName":"Sakai, Nobuko","creatorNameLang":"en"}]},{"creatorNames":[{"creatorName":"Suyama, Kazuhide","creatorNameLang":"en"}]},{"creatorNames":[{"creatorName":"Hosoya, Mitsuaki","creatorNameLang":"en"}]}]},"item_1617186499011":{"attribute_name":"Rights","attribute_value_mlt":[{"subitem_rights":"© 2014 The Fukushima Society of Medical Science","subitem_rights_language":"en"}]},"item_1617186609386":{"attribute_name":"Subject","attribute_value_mlt":[{"subitem_subject":"Systemic lupus erythematosus","subitem_subject_language":"en","subitem_subject_scheme":"Other"},{"subitem_subject":"Hemophagocytic syndrome","subitem_subject_language":"en","subitem_subject_scheme":"Other"},{"subitem_subject":"Autoimmune-associated hemophagocytic syndrome","subitem_subject_language":"en","subitem_subject_scheme":"Other"},{"subitem_subject":"Primary manifestation","subitem_subject_language":"en","subitem_subject_scheme":"Other"}]},"item_1617186626617":{"attribute_name":"Description","attribute_value_mlt":[{"subitem_description":"The primary manifestations of systemic lupus erythematosus (SLE) are various. One such manifestation is hemophagocytic syndrome (HPS). We here report a child with SLE presenting with HPS as a primary manifestation. In October 2010, an 11-year-old Japanese boy presented with pancytopenia, elevated liver enzymes, hyperferritinemia and hemophagocytosis due to macrophages in the bone marrow, and was diagnosed with HPS. A year later, he was found to have proteinuria and hematuria. Oral aphtha and Raynaud's phenomenon were observed, and the patient showed low serum complement levels and was positive for anti-nuclear antibodies (ANAs). He was subsequently diagnosed with SLE. Moreover, low serum complement levels and ANA positivity were detected in a serum sample preserved at the onset of HPS. The HPS was considered to be a primary manifestation of SLE on the basis of these findings. Based on this case, the presence of an underlying disease, such as SLE, should be investigated in cases of HPS.","subitem_description_language":"en","subitem_description_type":"Abstract"}]},"item_1617186643794":{"attribute_name":"Publisher","attribute_value_mlt":[{"subitem_publisher":"The Fukushima Society of Medical Science","subitem_publisher_language":"en"}]},"item_1617186702042":{"attribute_name":"Language","attribute_value_mlt":[{"subitem_language":"eng"}]},"item_1617186920753":{"attribute_name":"Source Identifier","attribute_value_mlt":[{"subitem_source_identifier":"0016-2590","subitem_source_identifier_type":"PISSN"},{"subitem_source_identifier":"2185-4610","subitem_source_identifier_type":"EISSN"},{"subitem_source_identifier":"AA0065246X","subitem_source_identifier_type":"NCID"}]},"item_1617187056579":{"attribute_name":"Bibliographic Information","attribute_value_mlt":[{"bibliographicIssueDates":{"bibliographicIssueDate":"2014","bibliographicIssueDateType":"Issued"},"bibliographicIssueNumber":"2","bibliographicPageEnd":"186","bibliographicPageStart":"181","bibliographicVolumeNumber":"60","bibliographic_titles":[{"bibliographic_title":"Fukushima Journal of Medical Science","bibliographic_titleLang":"en"}]}]},"item_1617258105262":{"attribute_name":"Resource Type","attribute_value_mlt":[{"resourcetype":"journal article","resourceuri":"http://purl.org/coar/resource_type/c_6501"}]},"item_1617265215918":{"attribute_name":"Version Type","attribute_value_mlt":[{"subitem_version_resource":"http://purl.org/coar/version/c_970fb48d4fbd8a85","subitem_version_type":"VoR"}]},"item_1617353299429":{"attribute_name":"Relation","attribute_value_mlt":[{"subitem_relation_type":"isIdenticalTo","subitem_relation_type_id":{"subitem_relation_type_id_text":"https://doi.org/10.5387/fms.2013-24","subitem_relation_type_select":"DOI"}},{"subitem_relation_type_id":{"subitem_relation_type_id_text":"25747608","subitem_relation_type_select":"PMID"}},{"subitem_relation_type_id":{"subitem_relation_type_id_text":"2016153998","subitem_relation_type_select":"ICHUSHI"}}]},"item_1617605131499":{"attribute_name":"File","attribute_type":"file","attribute_value_mlt":[{"accessrole":"open_access","date":[{"dateType":"Available","dateValue":"2015-07-06"}],"displaytype":"detail","filename":"FksmJMedSci_60_p181.pdf","filesize":[{"value":"786.3 KB"}],"format":"application/pdf","mimetype":"application/pdf","url":{"url":"https://fmu.repo.nii.ac.jp/record/2001877/files/FksmJMedSci_60_p181.pdf"},"version_id":"332323fb-6ddc-434a-bd52-0d59cb677aed"}]},"item_title":"A case of a child with sle presenting with hps as a primary manifestation","item_type_id":"40002","owner":"8","path":["1732874517304"],"pubdate":{"attribute_name":"PubDate","attribute_value":"2015-07-06"},"publish_date":"2015-07-06","publish_status":"0","recid":"2001877","relation_version_is_last":true,"title":["A case of a child with sle presenting with hps as a primary manifestation"],"weko_creator_id":"8","weko_shared_id":-1},"updated":"2024-11-29T10:28:55.078069+00:00"}