{"created":"2024-11-29T09:49:40.430019+00:00","id":2001836,"links":{},"metadata":{"_buckets":{"deposit":"07a86861-ff86-4124-a535-2d9ccc5879cf"},"_deposit":{"created_by":8,"id":"2001836","owners":[8],"pid":{"revision_id":0,"type":"depid","value":"2001836"},"status":"published"},"_oai":{"id":"oai:fmu.repo.nii.ac.jp:02001836","sets":["1732778801467:1732778962699:1732873412714"]},"author_link":[],"item_1617186331708":{"attribute_name":"Title","attribute_value_mlt":[{"subitem_title":"Two cases of mixed connective tissue disease complicated with thrombotic thrombocytopenic purpura","subitem_title_language":"en"}]},"item_1617186419668":{"attribute_name":"Creator","attribute_type":"creator","attribute_value_mlt":[{"creatorNames":[{"creatorName":"Suzuki, Eiji","creatorNameLang":"en"}]},{"creatorNames":[{"creatorName":"Kanno, Takashi","creatorNameLang":"en"}]},{"creatorNames":[{"creatorName":"Asano, Tomoyuki","creatorNameLang":"en"}]},{"creatorNames":[{"creatorName":"Tsutsumi, Akito","creatorNameLang":"en"}]},{"creatorNames":[{"creatorName":"Kobayashi, Hiroko","creatorNameLang":"en"}]},{"creatorNames":[{"creatorName":"Watanabe, Hiroshi","creatorNameLang":"en"}]},{"creatorNames":[{"creatorName":"Ohira, Hiromasa","creatorNameLang":"en"}]}]},"item_1617186499011":{"attribute_name":"Rights","attribute_value_mlt":[{"subitem_rights":"© 2013 The Fukushima Society of Medical Science","subitem_rights_language":"en"}]},"item_1617186609386":{"attribute_name":"Subject","attribute_value_mlt":[{"subitem_subject":"a disintegrin-like metalloproteinase with thrombospondin type 1 motifs 13 (ADAMTS13)","subitem_subject_language":"en","subitem_subject_scheme":"Other"},{"subitem_subject":"mixed connective tissue disease (MCTD)","subitem_subject_language":"en","subitem_subject_scheme":"Other"},{"subitem_subject":"pericardial effusion","subitem_subject_language":"en","subitem_subject_scheme":"Other"},{"subitem_subject":"thrombotic thrombocytopenic purpura (TTP)","subitem_subject_language":"en","subitem_subject_scheme":"Other"}]},"item_1617186626617":{"attribute_name":"Description","attribute_value_mlt":[{"subitem_description":"Thrombotic thrombocytopenic purpura (TTP) is a rare complication of connective tissue diseases. Here, we describe 2 patients with mixed connective tissue disease (MCTD) who had pericardial effusion and TTP. They had moderately low to normal ADAMTS13 activity and no ADAMTS13 neutralizing antibodies. Both patients responded poorly to plasma exchange. One patient died due to multiple organ failure and the other due to infection. Although rare, TTP is an important complication that leads to a poor prognosis in MCTD patients.","subitem_description_language":"en","subitem_description_type":"Abstract"}]},"item_1617186643794":{"attribute_name":"Publisher","attribute_value_mlt":[{"subitem_publisher":"The Fukushima Society of Medical Science","subitem_publisher_language":"en"}]},"item_1617186702042":{"attribute_name":"Language","attribute_value_mlt":[{"subitem_language":"eng"}]},"item_1617186920753":{"attribute_name":"Source Identifier","attribute_value_mlt":[{"subitem_source_identifier":"0016-2590","subitem_source_identifier_type":"PISSN"},{"subitem_source_identifier":"2185-4610","subitem_source_identifier_type":"EISSN"},{"subitem_source_identifier":"AA0065246X","subitem_source_identifier_type":"NCID"}]},"item_1617187056579":{"attribute_name":"Bibliographic Information","attribute_value_mlt":[{"bibliographicIssueDates":{"bibliographicIssueDate":"2013","bibliographicIssueDateType":"Issued"},"bibliographicIssueNumber":"1","bibliographicPageEnd":"55","bibliographicPageStart":"49","bibliographicVolumeNumber":"59","bibliographic_titles":[{"bibliographic_title":"Fukushima Journal of Medical Science","bibliographic_titleLang":"en"}]}]},"item_1617258105262":{"attribute_name":"Resource Type","attribute_value_mlt":[{"resourcetype":"journal article","resourceuri":"http://purl.org/coar/resource_type/c_6501"}]},"item_1617265215918":{"attribute_name":"Version Type","attribute_value_mlt":[{"subitem_version_resource":"http://purl.org/coar/version/c_970fb48d4fbd8a85","subitem_version_type":"VoR"}]},"item_1617353299429":{"attribute_name":"Relation","attribute_value_mlt":[{"subitem_relation_type":"isIdenticalTo","subitem_relation_type_id":{"subitem_relation_type_id_text":"https://doi.org/10.5387/fms.59.49","subitem_relation_type_select":"DOI"}},{"subitem_relation_type_id":{"subitem_relation_type_id_text":"23842515","subitem_relation_type_select":"PMID"}},{"subitem_relation_type_id":{"subitem_relation_type_id_text":"2014059601","subitem_relation_type_select":"ICHUSHI"}}]},"item_1617605131499":{"attribute_name":"File","attribute_type":"file","attribute_value_mlt":[{"accessrole":"open_access","date":[{"dateType":"Available","dateValue":"2013-08-15"}],"displaytype":"detail","filename":"FksmJMedSci_59_p49.pdf","filesize":[{"value":"354.0 KB"}],"format":"application/pdf","mimetype":"application/pdf","url":{"url":"https://fmu.repo.nii.ac.jp/record/2001836/files/FksmJMedSci_59_p49.pdf"},"version_id":"62a698e4-60d5-4d25-81fb-49a3cf5e446a"}]},"item_title":"Two cases of mixed connective tissue disease complicated with thrombotic thrombocytopenic purpura","item_type_id":"40002","owner":"8","path":["1732873412714"],"pubdate":{"attribute_name":"PubDate","attribute_value":"2013-08-15"},"publish_date":"2013-08-15","publish_status":"0","recid":"2001836","relation_version_is_last":true,"title":["Two cases of mixed connective tissue disease complicated with thrombotic thrombocytopenic purpura"],"weko_creator_id":"8","weko_shared_id":-1},"updated":"2024-11-29T09:55:21.228382+00:00"}